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Influence of wheelchair positioning aids on the respiratory function of patients with Duchenne muscular dystrophy. The purpose of this study was to determine the influence of wheelchair positioning aids on the respiratory function of patients with Duchenne muscular dystrophy DMD.

Twelve non-ambulatory DMD patients, between 10 to 22 years of age, were evaluated. They were assessed in their adapted wheelchairs and in a standard wheelchair without tilt or reclining. The wheelchairs of the participants possessed adaptations in the backrest and the seat, made according to the specifics of each patient.

For data analysis we used the paired t-test adopting the significance level of 0. The positioning aids resulted in statistically significant better values of all respiratory parameters: MV 8, These results may suggest that wheelchair positioning aids can positively influence pulmonary function for non-ambulatory DMD patients. Keywords: Duchenne muscular dystrophy; wheelchairs; respiratory system; posture.

Kurz et al. Na mesma linha, os resultados de Yamashita et al. A PImax foi mensurada a partir do volume residual e a PEmax da capacidade pulmonar total, mantidas por 3 s.

Nessa linha, o presente estudo procurou avaliar se o mesmo ocorre em pacientes com DMD quando dependentes de cadeira de rodas. Managing Duchenne muscular dystrophy -- the additive effect of spinal surgery and home nocturnal ventilation in improving survival.

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Brazilian Consensus on Duchenne Muscular Dystrophy. Part 2: Rehabilitation and Systemic Care

Significant advances in the understanding and management of Duchenne muscular dystrophy DMD have occurred since the publication of international guidelines for DMD care in Our objective was to provide an evidence-based national consensus statement for multidisciplinary care of DMD in Brazil. A combination of the Delphi technique with a systematic review of studies from to was employed to classify evidence levels and grade of recommendations for the guideline. Our recommendations were divided in two parts. Guideline methodology and overall disease concept descriptions are found in Part 1. Here we present Part 2, where we provide the results and recommendations on rehabilitation and systemic care for DMD.


Distrofia muscular

E-mail: lucordeiro. Foram encontrados registros e, destes, selecionados Recomenda-se usar a Egen Klassifikation, a North Star Ambulatory Assessment e fazer o teste de caminhada de seis minutos. Se encontraron registros, de los cuales se seleccionaron Se recomienda emplear la Egen Klassifikation, la North Star Ambulatory Assessment y aplicar la prueba de caminata de seis minutos. The aim of this study is to map the use of aquatic physical therapy in individuals with muscular dystrophy, to characterize aquatic physical therapy intervention and identify measured components variables and measurement instruments used by the studies.

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