Epidermolysis bullosa acquisita: literature review. Ann Dermatol Venereol. Epidermolysis bullosa acquisita: report of three cases and review of all published cases. Arch Dermatol. Epidermolysis bullosa acquisita: ultrastructural and immunological studies.
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These images are a random sampling from a Bing search on the term "Epidermolysis Bullosa Acquisita. Search Bing for all related images. Started in , this collection now contains interlinked topic pages divided into a tree of 31 specialty books and chapters. Content is updated monthly with systematic literature reviews and conferences.
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Toggle navigation. VesiculoBullous Disorders Chapter. From Related Chapters. Page Contents Epidemiology Mean age of onset: 50 years. Pathophysiology Autoimmune Subepidermal Blister ing condition. Signs Trauma prone areas more commonly affected Tense Blister s and erosions over extensor surfaces Knuckles Dorsal hands Elbow s Knee s Ankle s Mucosal involvement common Oral, nasal, and esophageal mucosa Conjunctiva l mucosa.
Labs Histology Subepidermal Blister with inflammatory infiltrate Immunofluorescence IgG deposits at dermal-epidermal junction. Complications Scarring skin lesions with associated milia. Course Chronic waxing and waning course. Images: Related links to external sites from Bing. Related Studies. Trip Database TrendMD. Ontology: Epidermolysis Bullosa C Epidermolysis bullosa is inherited and usually starts at birth. Patients with epidermolysis bullosa may be at increased risk of squamous cell cancer of the skin.
Definition NCI An autosomal recessive inherited skin disorder caused by mutations in the genes encoding keratins 5 and 14, collagen VII or laminin 5. It is characterized by skin fragility and the formation of blisters. The blisters may become large and ulcerated, resulting in skin infections and loss of body fluids. Definition MSH Group of genetically determined disorders characterized by the blistering of skin and mucosae.
There are four major forms: acquired, simple, junctional, and dystrophic. Each of the latter three has several varieties. Definition CSP inherited chronic noninflammatory skin disease manifested by vesicles, large bullae blisters , and skin erosions which often result from trauma. Ontology: Epidermolysis Bullosa Acquisita C Definition NCI A chronic autoimmune inflammatory disorder characterized by the formation of subepidermal blisters in the skin and the mucous membranes.
Related Topics in VesiculoBullous Disorders. Dermatology Chapters. Dermatology - VesiculoBullous Disorders Pages.
Back Links pages that link to this page. Hypertrichosis Pemphigoid Cicatricial Pemphigoid Blister. Search other sites for 'Epidermolysis Bullosa Acquisita'. A group of chronic skin disorders in which fluid-filled blisters form on the skin and mucosa the moist, inner lining of some organs and body cavities. An autosomal recessive inherited skin disorder caused by mutations in the genes encoding keratins 5 and 14, collagen VII or laminin 5.
Group of genetically determined disorders characterized by the blistering of skin and mucosae. Q81 , Q Acantolisi bollosa , Epidermolisi bollosa. Epidermolysis bullosa, nicht naeher bezeichnet , Acantholysis bullosa , Epidermolysis bullosa hereditaria , Epidermolysis bullosa. Epidermolysis bullosa , Bulozna epidermoliza. A chronic autoimmune inflammatory disorder characterized by the formation of subepidermal blisters in the skin and the mucous membranes.
Form of epidermolysis bullosa characterized by trauma-induced, subepidermal blistering with no family history of the disease. Disease or Syndrome T Epidermolysis bullosa acquisita.
Hankinnainen rakkulainen epidermolyysi. Erworbene Epidermolysis bullosa , Epidermolysis bullosa acquisita , Epidermolysis bullosa, erworbene. Szerzett epidermolysis bullosa. Epidermolysis bullosa acquisita , Ervervet epidermolysis bullosa. Epidermolisi bollosa acquisita.
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Only comments seeking to improve the quality and accuracy of information on the Orphanet website are accepted. For all other comments, please send your remarks via contact us. Only comments written in English can be processed. A rare, chronic, incurable, sub epithelial autoimmune bullous disease characterized by the presence of tissue bound autoantibodies against type VII collagen within the basement membrane zone of the dermal-epidermal junction of stratified squamous epithelia. The patient's serum may also have anti-type VII collagen autoantibodies. The clinical presentation is varied, and may involve the skin, oral mucosa and the upper third of the esophagus.
Epidermolisis ampollosa adquirida y mieloma múltiple